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KMID : 1103720220830030744
Journal of the Korean Society of Radiology
2022 Volume.83 No. 3 p.744 ~ p.749
Fibrosing Mediastinits Causing Obstruction of Left Lower Lobar Bronchus: A Pediatric Case Report
Sim Young-Woo

Kim Young-Seon
Lee Seung-Eun
Jang Min-Hye
Abstract
Fibrosing mediastinitis is a rare benign disorder characterized by the proliferation of dense fibrous tissue within the mediastinum. It typically manifests as localized or infiltrative soft-tissue masses in the middle mediastinum or hilar area, which cause compression and encasement of adjacent mediastinal structures, such as the vessels or airway. Here, we report a rare case of fibrosing mediastinitis in a 13-year-old girl that presented as a middle mediastinal mass lesion on CT scan with obliterating left lower lobar bronchus. The patient¡¯s symptoms and follow-up chest CT showed significant improvement following systemic corticosteroid treatment. As fibrosing mediastinitis can improve with systemic steroid therapy, radiologists must be aware of its radiologic findings when discriminating between infiltrating soft tissue lesions in the mediastinum.
KEYWORD
Computed Tomography, X-Ray, Mediastinal Fibrosis, Sclerosing Mediastinitis
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